Best management in isolated right ventricular hypoplasia with septal defects in adults

Khajali, Zahra and Arabian, Maedeh and Aliramezany, Maryam (2020) Best management in isolated right ventricular hypoplasia with septal defects in adults. Journal of Cardiovascular and Thoracic Research, 12 (3). pp. 214-220. ISSN 2008-5117

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Abstract

Hypoplastic right ventricle is a rare congenital disease usually associated with pulmonary atresia or tricuspid atresia. Isolated right ventricular hypoplasia is a rare anomaly without important valvular abnormalities. It is associated with inter atrial septal defects leading to the right-to-left shunting of blood. Patients with isolated right ventricular hypoplasia usually have different and variable courses. In some patients, it is recognized in the perinatal period and necessitates prompt intervention; nonetheless, there are some reports of this anomaly in old age with no significant symptoms. In this report, we describe the clinical data and management of 6 adult cases with isolated right ventricular hypoplasia treated medically or surgically based on the severity of the disease and symptoms and then offer an in-depth discussion regarding this rare anomaly.

Item Type: Article
Subjects: Research Asian Plos > Medical Science
Depositing User: Unnamed user with email support@research.asianplos.com
Date Deposited: 05 May 2023 11:49
Last Modified: 18 Oct 2024 05:07
URI: http://abstract.stmdigitallibrary.com/id/eprint/740

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